Postoperative full abduction in a patient of Duane retraction syndrome without an abducens nerve: a case report
نویسندگان
چکیده
BACKGROUND Duane retraction syndrome (DRS) consists of abduction deficit, globe retraction and upshoots or downshoots with adduction. The abducens nerve on the affected side is absent in type 1 DRS. After bilateral medial rectus muscle recession in unilateral type 1 DRS may improve the abduction limitation, but still more than -3 limitation remains. CASE PRESENTATION A 6-month-old boy presented with esotropia which had been noticed in early infancy. He showed limited abduction, fissure narrowing on attempted adduction and a small upshoot OS. Left abducens nerve was not identified on magnetic resonance imaging compatible with Duane retraction syndrome type 1. He showed full abduction after bilateral medial rectus recession of 6.0 mm at the age of 9 months, and remained orthotropia with full abduction OU 2 years postoperatively. He is my only patient with Duane retraction syndrome who showed full abduction after bilateral medial rectus recession. CONCLUSIONS A patient with the type 1 Duane retraction syndrome rarely may show full abduction after bilateral medial rectus recession mimicking infantile esotropia.
منابع مشابه
Congenital sixth nerve palsy with associated anomalies
Congenital abduction deficit is most likely due to Duane's retraction syndrome as congenital abducens nerve palsy is very rare. We report two cases of infantile abduction deficit due to sixth nerve palsy associated with other anomalies to highlight the importance of including neuroimaging in the evaluation of an infant presenting with a limitation of abduction.
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OBJECTIVE To describe our results using augmented temporal superior rectus transposition (SRT) with adjustable medial rectus muscle recession (MRc) for treatment of Duane syndrome and sixth nerve palsy. METHODS Retrospective surgical case review of patients undergoing SRT. Preoperative and postoperative orthoptic measurements were recorded. Minimum follow-up was 6 weeks. Main outcome measures...
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BACKGROUND AND PURPOSE Duane's retraction syndrome (DRS) consists of a congenital abduction deficit of the eyeball accompanied by retraction of the globe on attempted adduction and by upshoots or downshoots of the affected eye on adduction. These characteristic diagnostic signs of DRS, however, might not be manifested in early childhood. We evaluated the usefulness of MR imaging as a diagnostic...
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Duane (I905) emphasized six features of a characteristic congenital ocular motility syndrome: (i) Complete, or less often partial, loss of abduction of the affected eye; (2) Partial, or rarely complete, restriction of adduction of the aHected eye; (3) Retraction of the affected eye into the orbit on adduction; (4) Oblique overshoot of the affected eye either up and in or down and in on adductio...
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